Matches in DBpedia 2014 for { ?s ?p Glycogen storage disease type I (GSD I) or von Gierke's disease, is the most common of the glycogen storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase, and has an incidence in the American population of approximately 1 in 50,000 to 100,000 births.The deficiency impairs the ability of the liver to produce free glucose from glycogen and from gluconeogenesis.. }
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- Glycogen_storage_disease_type_I comment "Glycogen storage disease type I (GSD I) or von Gierke's disease, is the most common of the glycogen storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase, and has an incidence in the American population of approximately 1 in 50,000 to 100,000 births.The deficiency impairs the ability of the liver to produce free glucose from glycogen and from gluconeogenesis.".