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- Caroli_disease abstract "Caroli disease is a rare inherited disorder characterized by dilatation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by ectasia. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal hypertension and congenital hepatic fibrosis. The differences between the causes of the two cases have not yet been discovered. Caroli disease is also associated with liver failure and polycystic kidney disease. The disease affects about 1 in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease.Caroli disease also is known as communicating cavernous ectasia, or congenital cystic dilatation of the intrahepatic biliary tree. Caroli disease is distinct from other diseases that cause ductal dilatation caused by obstruction, in that it is not one of the many choledochal cyst derivatives.".
- Caroli_disease diseasesdb "29874".
- Caroli_disease emedicineSubject "radio".
- Caroli_disease emedicineTopic "131".
- Caroli_disease meshId "D016767".
- Caroli_disease omim "263200".
- Caroli_disease thumbnail BiliaryTract.gif?width=300.
- Caroli_disease wikiPageID "308573".
- Caroli_disease wikiPageRevisionID "594333685".
- Caroli_disease caption "Figure 1 Bilary tract, system, or tree includes the gallbladder and the bile ducts.".
- Caroli_disease diseasesdb "29874".
- Caroli_disease emedicinesubj "radio".
- Caroli_disease emedicinetopic "131".
- Caroli_disease hasPhotoCollection Caroli_disease.
- Caroli_disease meshid "D016767".
- Caroli_disease name "Caroli disease".
- Caroli_disease omim "263200".
- Caroli_disease wordnet_type synset-disease-noun-1.
- Caroli_disease subject Category:Biliary_tract_disorders.
- Caroli_disease subject Category:Ciliopathy.
- Caroli_disease subject Category:Hepatology.
- Caroli_disease subject Category:Rare_diseases.
- Caroli_disease type Abstraction100002137.
- Caroli_disease type Attribute100024264.
- Caroli_disease type BiliaryTractDisorders.
- Caroli_disease type Condition113920835.
- Caroli_disease type Disease114070360.
- Caroli_disease type Disorder114052403.
- Caroli_disease type IllHealth114052046.
- Caroli_disease type Illness114061805.
- Caroli_disease type PathologicalState114051917.
- Caroli_disease type PhysicalCondition114034177.
- Caroli_disease type State100024720.
- Caroli_disease type Disease.
- Caroli_disease type AilmentCondition.
- Caroli_disease type Situation.
- Caroli_disease comment "Caroli disease is a rare inherited disorder characterized by dilatation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by ectasia. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal hypertension and congenital hepatic fibrosis. The differences between the causes of the two cases have not yet been discovered.".
- Caroli_disease label "Caroli disease".
- Caroli_disease label "Caroli-Syndrom".
- Caroli_disease label "Choroba Carolego".
- Caroli_disease label "Enfermedad de Caroli".
- Caroli_disease label "Maladie de Caroli".
- Caroli_disease label "Malattia di Caroli".
- Caroli_disease label "Синдром Кароли".
- Caroli_disease sameAs Caroli-Syndrom.
- Caroli_disease sameAs Enfermedad_de_Caroli.
- Caroli_disease sameAs Maladie_de_Caroli.
- Caroli_disease sameAs Malattia_di_Caroli.
- Caroli_disease sameAs Choroba_Carolego.
- Caroli_disease sameAs m.01swc6.
- Caroli_disease sameAs Q1044327.
- Caroli_disease sameAs Q1044327.
- Caroli_disease sameAs Caroli_disease.
- Caroli_disease wasDerivedFrom Caroli_disease?oldid=594333685.
- Caroli_disease depiction BiliaryTract.gif.
- Caroli_disease isPrimaryTopicOf Caroli_disease.
- Caroli_disease name "Caroli disease".