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- Glycogen_debranching_enzyme abstract "A debranching enzyme is a molecule that helps facilitate the breakdown of glycogen, which serves as a store of glucose in the body, through glucosyltransferase and glucosidase activity. Together with phosphorylases, debranching enzymes mobilize glucose reserves from glycogen deposits in the muscles and liver. This constitutes a major source of energy reserves in most organisms. Glycogen breakdown is highly regulated in the body, especially in the liver, by various hormones including insulin and glucagon, to maintain a homeostatic balance of blood-glucose levels. When glycogen breakdown is compromised by mutations in the glycogen debranching enzyme, metabolic diseases such as Glycogen storage disease type III can result.Glucosyltransferase and glucosidase are performed by a single enzyme in mammals, yeast, and some bacteria, but by two distinct enzymes in E. coli and other bacteria, complicating nomenclature. Proteins that catalyze both functions are referred to as glycogen debranching enzymes (GDEs). When glucosyltransferase and glucosidase are catalyzed by distinct enzymes, "glycogen debranching enzyme" usually refers to the glucosidase enzyme. In some literature, an enzyme capable only of glucosidase is referred to as a "debranching enzyme".".
- Glycogen_debranching_enzyme entrezgene "178".
- Glycogen_debranching_enzyme thumbnail Glycogen_Debranching_Enzyme.png?width=300.
- Glycogen_debranching_enzyme wikiPageExternalLink br.fcgi?book=gene&part=gsd3.
- Glycogen_debranching_enzyme wikiPageExternalLink 232400,610860,232400,610860.
- Glycogen_debranching_enzyme wikiPageID "2940689".
- Glycogen_debranching_enzyme wikiPageRevisionID "591478352".
- Glycogen_debranching_enzyme casNumber "9012".
- Glycogen_debranching_enzyme casNumber "9032-09-01".
- Glycogen_debranching_enzyme colwidth "35".
- Glycogen_debranching_enzyme ecNumber "2.4".
- Glycogen_debranching_enzyme ecNumber "3.2".
- Glycogen_debranching_enzyme goCode "4134".
- Glycogen_debranching_enzyme goCode "4135".
- Glycogen_debranching_enzyme hasPhotoCollection Glycogen_debranching_enzyme.
- Glycogen_debranching_enzyme iubmbEcNumber "2".
- Glycogen_debranching_enzyme iubmbEcNumber "3".
- Glycogen_debranching_enzyme name "4".
- Glycogen_debranching_enzyme name "amylo-α-1,6-glucosidase".
- Glycogen_debranching_enzyme subject Category:EC_2.4.1.
- Glycogen_debranching_enzyme subject Category:EC_3.2.1.
- Glycogen_debranching_enzyme type Biomolecule.
- Glycogen_debranching_enzyme type Protein.
- Glycogen_debranching_enzyme type ProteinMolecule.
- Glycogen_debranching_enzyme type BiologicalObject.
- Glycogen_debranching_enzyme comment "A debranching enzyme is a molecule that helps facilitate the breakdown of glycogen, which serves as a store of glucose in the body, through glucosyltransferase and glucosidase activity. Together with phosphorylases, debranching enzymes mobilize glucose reserves from glycogen deposits in the muscles and liver. This constitutes a major source of energy reserves in most organisms.".
- Glycogen_debranching_enzyme label "Enzyme de débranchement du glycogène".
- Glycogen_debranching_enzyme label "Glycogen debranching enzyme".
- Glycogen_debranching_enzyme label "Glykogen-Debranching-Enzym".
- Glycogen_debranching_enzyme sameAs Glykogen-Debranching-Enzym.
- Glycogen_debranching_enzyme sameAs Enzyme_de_débranchement_du_glycogène.
- Glycogen_debranching_enzyme sameAs m.08f1vm.
- Glycogen_debranching_enzyme sameAs Q1532471.
- Glycogen_debranching_enzyme sameAs Q1532471.
- Glycogen_debranching_enzyme wasDerivedFrom Glycogen_debranching_enzyme?oldid=591478352.
- Glycogen_debranching_enzyme depiction Glycogen_Debranching_Enzyme.png.
- Glycogen_debranching_enzyme isPrimaryTopicOf Glycogen_debranching_enzyme.