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- Guanidinoacetate_N-methyltransferase abstract "Guanidinoacetate N-methyltransferase (EC 2.1.1.2) is an enzyme that catalyzes the chemical reaction and is encoded by gene GAMT located on chromosome 19p13.3.S-adenosyl-L-methionine + guanidinoacetate S-adenosyl-L-homocysteine + creatineThus, the two substrates of this enzyme are S-adenosyl methionine and guanidinoacetate, whereas its two products are S-adenosylhomocysteine and creatine.This enzyme belongs to the family of transferases, specifically those transferring one-carbon group methyltransferases. The systematic name of this enzyme class is S-adenosyl-L-methionine:N-guanidinoacetate methyltransferase. Other names in common use include GA methylpherase, guanidinoacetate methyltransferase, guanidinoacetate transmethylase, methionine-guanidinoacetic transmethylase, and guanidoacetate methyltransferase. This enzyme participates in glycine, serine and threonine metabolism and arginine and proline metabolism. The protein encoded by this gene is a methyltransferase that converts guanidoacetate to creatine, using S-adenosylmethionine as the methyl donor. Defects in this gene have been implicated in neurologic syndromes and muscular hypotonia, probably due to creatine deficiency and accumulation of guanidinoacetate in the brain of affected individuals. Two transcript variants encoding different isoforms have been described for this gene.".
- Guanidinoacetate_N-methyltransferase entrezgene "2593".
- Guanidinoacetate_N-methyltransferase wikiPageID "14024420".
- Guanidinoacetate_N-methyltransferase wikiPageRevisionID "551383510".
- Guanidinoacetate_N-methyltransferase casNumber "9029".
- Guanidinoacetate_N-methyltransferase ecNumber "2.1".
- Guanidinoacetate_N-methyltransferase goCode "30731".
- Guanidinoacetate_N-methyltransferase hasPhotoCollection Guanidinoacetate_N-methyltransferase.
- Guanidinoacetate_N-methyltransferase iubmbEcNumber "2".
- Guanidinoacetate_N-methyltransferase name "guanidinoacetate N-methyltransferase".
- Guanidinoacetate_N-methyltransferase requireManualInspection "no".
- Guanidinoacetate_N-methyltransferase updateCitations "yes".
- Guanidinoacetate_N-methyltransferase updatePage "yes".
- Guanidinoacetate_N-methyltransferase updateProteinBox "yes".
- Guanidinoacetate_N-methyltransferase updateSummary "yes".
- Guanidinoacetate_N-methyltransferase subject Category:EC_2.1.1.
- Guanidinoacetate_N-methyltransferase subject Category:Enzymes_of_known_structure.
- Guanidinoacetate_N-methyltransferase type Abstraction100002137.
- Guanidinoacetate_N-methyltransferase type Activator114723079.
- Guanidinoacetate_N-methyltransferase type Catalyst114723628.
- Guanidinoacetate_N-methyltransferase type Chemical114806838.
- Guanidinoacetate_N-methyltransferase type Compound114818238.
- Guanidinoacetate_N-methyltransferase type Enzyme114732946.
- Guanidinoacetate_N-methyltransferase type EnzymesOfKnownStructure.
- Guanidinoacetate_N-methyltransferase type Macromolecule114944888.
- Guanidinoacetate_N-methyltransferase type Material114580897.
- Guanidinoacetate_N-methyltransferase type Matter100020827.
- Guanidinoacetate_N-methyltransferase type Molecule114682133.
- Guanidinoacetate_N-methyltransferase type OrganicCompound114727670.
- Guanidinoacetate_N-methyltransferase type Part113809207.
- Guanidinoacetate_N-methyltransferase type PhysicalEntity100001930.
- Guanidinoacetate_N-methyltransferase type Protein114728724.
- Guanidinoacetate_N-methyltransferase type Relation100031921.
- Guanidinoacetate_N-methyltransferase type Substance100019613.
- Guanidinoacetate_N-methyltransferase type Thing100002452.
- Guanidinoacetate_N-methyltransferase type Unit109465459.
- Guanidinoacetate_N-methyltransferase type Biomolecule.
- Guanidinoacetate_N-methyltransferase type Protein.
- Guanidinoacetate_N-methyltransferase type BiologicalObject.
- Guanidinoacetate_N-methyltransferase comment "Guanidinoacetate N-methyltransferase (EC 2.1.1.2) is an enzyme that catalyzes the chemical reaction and is encoded by gene GAMT located on chromosome 19p13.3.S-adenosyl-L-methionine + guanidinoacetate S-adenosyl-L-homocysteine + creatineThus, the two substrates of this enzyme are S-adenosyl methionine and guanidinoacetate, whereas its two products are S-adenosylhomocysteine and creatine.This enzyme belongs to the family of transferases, specifically those transferring one-carbon group methyltransferases. ".
- Guanidinoacetate_N-methyltransferase label "Guanidinoacetat-N-Methyltransferase".
- Guanidinoacetate_N-methyltransferase label "Guanidinoacetate N-methyltransferase".
- Guanidinoacetate_N-methyltransferase label "Guanidinoacetato N-metiltransferasi".
- Guanidinoacetate_N-methyltransferase label "グアニジノ酢酸-N-メチルトランスフェラーゼ".
- Guanidinoacetate_N-methyltransferase sameAs Guanidinoacetat-N-Methyltransferase.
- Guanidinoacetate_N-methyltransferase sameAs Guanidinoacetato_N-metiltransferasi.
- Guanidinoacetate_N-methyltransferase sameAs グアニジノ酢酸-N-メチルトランスフェラーゼ.
- Guanidinoacetate_N-methyltransferase sameAs m.03crb8r.
- Guanidinoacetate_N-methyltransferase sameAs Q408303.
- Guanidinoacetate_N-methyltransferase sameAs Q408303.
- Guanidinoacetate_N-methyltransferase sameAs GAMT.
- Guanidinoacetate_N-methyltransferase sameAs 3360.
- Guanidinoacetate_N-methyltransferase sameAs 624.
- Guanidinoacetate_N-methyltransferase sameAs Guanidinoacetate_N-methyltransferase.
- Guanidinoacetate_N-methyltransferase wasDerivedFrom Guanidinoacetate_N-methyltransferase?oldid=551383510.
- Guanidinoacetate_N-methyltransferase isPrimaryTopicOf Guanidinoacetate_N-methyltransferase.