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- Paroxysmal_nocturnal_hemoglobinuria abstract "Paroxysmal nocturnal hemoglobinuria (PNH), sometimes referred to as Marchiafava-Micheli syndrome, is a rare, genetically acquired, life-threatening disease of the blood characterized by complement-induced intravascular hemolytic anemia (anemia due to destruction of red blood cells in the bloodstream), red urine (due to the appearance of hemoglobin in the urine) and thrombosis.PNH is the only hemolytic anemia which is most often caused by an acquired (rather than inherited) intrinsic defect in the cell membrane (deficiency of glycophosphatidylinositol leading to absence of protective proteins on the membrane). It may develop on its own ("primary PNH") or in the context of other bone marrow disorders such as aplastic anemia ("secondary PNH"). Only a minority (26%) have the telltale red urine in the morning that originally gave the condition its name.Allogeneic bone marrow transplantation is the only curative therapy, but has significant rates of both mortality and ongoing morbidity. The monoclonal antibody eculizumab (Soliris) is effective at reducing the need for blood transfusions, improving quality of life, and reducing the risk of thrombosis.".
- Paroxysmal_nocturnal_hemoglobinuria diseasesdb "9688".
- Paroxysmal_nocturnal_hemoglobinuria emedicineSubject "med".
- Paroxysmal_nocturnal_hemoglobinuria emedicineTopic "2696".
- Paroxysmal_nocturnal_hemoglobinuria icd10 "D59.5".
- Paroxysmal_nocturnal_hemoglobinuria icd9 "283.2".
- Paroxysmal_nocturnal_hemoglobinuria medlineplus "000534".
- Paroxysmal_nocturnal_hemoglobinuria meshId "D006457".
- Paroxysmal_nocturnal_hemoglobinuria omim "300818".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.aamds.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnh-alliance.org.uk.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnhfoundation.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageExternalLink www.pnhinterestgroup.org.
- Paroxysmal_nocturnal_hemoglobinuria wikiPageID "513180".
- Paroxysmal_nocturnal_hemoglobinuria wikiPageRevisionID "604922538".
- Paroxysmal_nocturnal_hemoglobinuria diseasesdb "9688".
- Paroxysmal_nocturnal_hemoglobinuria emedicinesubj "med".
- Paroxysmal_nocturnal_hemoglobinuria emedicinetopic "2696".
- Paroxysmal_nocturnal_hemoglobinuria hasPhotoCollection Paroxysmal_nocturnal_hemoglobinuria.
- Paroxysmal_nocturnal_hemoglobinuria icd "283.2".
- Paroxysmal_nocturnal_hemoglobinuria icd "D59.5".
- Paroxysmal_nocturnal_hemoglobinuria medlineplus "534".
- Paroxysmal_nocturnal_hemoglobinuria meshid "D006457".
- Paroxysmal_nocturnal_hemoglobinuria name "Paroxysmal nocturnal hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria omim "300818".
- Paroxysmal_nocturnal_hemoglobinuria wordnet_type synset-disease-noun-1.
- Paroxysmal_nocturnal_hemoglobinuria subject Category:Acquired_hemolytic_anemia.
- Paroxysmal_nocturnal_hemoglobinuria subject Category:Rare_diseases.
- Paroxysmal_nocturnal_hemoglobinuria subject Category:Vascular-related_cutaneous_conditions.
- Paroxysmal_nocturnal_hemoglobinuria type Abstraction100002137.
- Paroxysmal_nocturnal_hemoglobinuria type Attribute100024264.
- Paroxysmal_nocturnal_hemoglobinuria type Condition113920835.
- Paroxysmal_nocturnal_hemoglobinuria type Disease114070360.
- Paroxysmal_nocturnal_hemoglobinuria type Disorder114052403.
- Paroxysmal_nocturnal_hemoglobinuria type IllHealth114052046.
- Paroxysmal_nocturnal_hemoglobinuria type Illness114061805.
- Paroxysmal_nocturnal_hemoglobinuria type PathologicalState114051917.
- Paroxysmal_nocturnal_hemoglobinuria type PhospholipidMetabolismDisorders.
- Paroxysmal_nocturnal_hemoglobinuria type PhysicalCondition114034177.
- Paroxysmal_nocturnal_hemoglobinuria type State100024720.
- Paroxysmal_nocturnal_hemoglobinuria type Vascular-relatedCutaneousConditions.
- Paroxysmal_nocturnal_hemoglobinuria type Disease.
- Paroxysmal_nocturnal_hemoglobinuria type AilmentCondition.
- Paroxysmal_nocturnal_hemoglobinuria type Situation.
- Paroxysmal_nocturnal_hemoglobinuria comment "Paroxysmal nocturnal hemoglobinuria (PNH), sometimes referred to as Marchiafava-Micheli syndrome, is a rare, genetically acquired, life-threatening disease of the blood characterized by complement-induced intravascular hemolytic anemia (anemia due to destruction of red blood cells in the bloodstream), red urine (due to the appearance of hemoglobin in the urine) and thrombosis.PNH is the only hemolytic anemia which is most often caused by an acquired (rather than inherited) intrinsic defect in the cell membrane (deficiency of glycophosphatidylinositol leading to absence of protective proteins on the membrane). ".
- Paroxysmal_nocturnal_hemoglobinuria label "Emoglobinuria parossistica notturna".
- Paroxysmal_nocturnal_hemoglobinuria label "Hemoglobinuria nocturna paroxística".
- Paroxysmal_nocturnal_hemoglobinuria label "Hemoglobinúria paroxística noturna".
- Paroxysmal_nocturnal_hemoglobinuria label "Hémoglobinurie paroxystique nocturne".
- Paroxysmal_nocturnal_hemoglobinuria label "Napadowa nocna hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria label "Paroxismale nachtelijke hemoglobinurie".
- Paroxysmal_nocturnal_hemoglobinuria label "Paroxysmal nocturnal hemoglobinuria".
- Paroxysmal_nocturnal_hemoglobinuria label "Paroxysmale nächtliche Hämoglobinurie".
- Paroxysmal_nocturnal_hemoglobinuria label "بيلة هيمغلوبينية انتيابية ليلية".
- Paroxysmal_nocturnal_hemoglobinuria label "発作性夜間血色素尿症".
- Paroxysmal_nocturnal_hemoglobinuria sameAs Paroxysmale_nächtliche_Hämoglobinurie.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Hemoglobinuria_nocturna_paroxística.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Hémoglobinurie_paroxystique_nocturne.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Emoglobinuria_parossistica_notturna.
- Paroxysmal_nocturnal_hemoglobinuria sameAs 発作性夜間血色素尿症.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Paroxismale_nachtelijke_hemoglobinurie.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Napadowa_nocna_hemoglobinuria.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Hemoglobinúria_paroxística_noturna.
- Paroxysmal_nocturnal_hemoglobinuria sameAs m.02k828.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Q1479494.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Q1479494.
- Paroxysmal_nocturnal_hemoglobinuria sameAs 1245.
- Paroxysmal_nocturnal_hemoglobinuria sameAs 3551.
- Paroxysmal_nocturnal_hemoglobinuria sameAs Paroxysmal_nocturnal_hemoglobinuria.
- Paroxysmal_nocturnal_hemoglobinuria wasDerivedFrom Paroxysmal_nocturnal_hemoglobinuria?oldid=604922538.
- Paroxysmal_nocturnal_hemoglobinuria isPrimaryTopicOf Paroxysmal_nocturnal_hemoglobinuria.
- Paroxysmal_nocturnal_hemoglobinuria name "Paroxysmal nocturnal hemoglobinuria".