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- Brown–Vialetto–Van_Laere_syndrome abstract "Brown-Vialetto-Van-Laere syndrome (BVVL), sometimes better known as Brown's Syndrome, is a rare degenerative disorder that is characterized by progressive sensorineural deafness (Voudris 2002). BVVL is marked by a number of cranial nerve palsies including those of the motor components involving the 7th and 9th-12th cranial nerves, spinal motor nerves, and upper motor neurons (Voudris 2002). The neurological manifestations develop insidiously: they usually begin with sensorineural deafness, progress inexorably to paralysis, and often culminate in respiratory failure. The syndrome affects children, adolescents, and younger adults; the age at onset of symptoms in the reported cases has ranged from infancy to the third decade of life. The prognosis is poor—most patients diagnosed with the syndrome die within 10 years. There is no cure.".
- Brown–Vialetto–Van_Laere_syndrome wikiPageID "19310838".
- Brown–Vialetto–Van_Laere_syndrome wikiPageRevisionID "603743648".
- Brown–Vialetto–Van_Laere_syndrome diseasesdb "32666".
- Brown–Vialetto–Van_Laere_syndrome id "Dipti2005".
- Brown–Vialetto–Van_Laere_syndrome id "Hiroshi2005".
- Brown–Vialetto–Van_Laere_syndrome id "Nair2006".
- Brown–Vialetto–Van_Laere_syndrome id "Prabhu2005".
- Brown–Vialetto–Van_Laere_syndrome id "Sathasivam2000".
- Brown–Vialetto–Van_Laere_syndrome id "Voudris2002".
- Brown–Vialetto–Van_Laere_syndrome id "Wilson1909".
- Brown–Vialetto–Van_Laere_syndrome name "Brown–Vialetto–Van Laere syndrome".
- Brown–Vialetto–Van_Laere_syndrome omim "211530".
- Brown–Vialetto–Van_Laere_syndrome reference "Dipti S et al. Brown-Vialetto-Van Laere syndrome; variability in age at onset and disease progression highlighting the phenotypic overlap with Fazio-Londe disease. Brain and Development. 27: 443-446.".
- Brown–Vialetto–Van_Laere_syndrome reference "Hiroshi N et al. A case of Brown-Vialetto-van Laere in Japan. Clinical Neurology. 45:357-361.".
- Brown–Vialetto–Van_Laere_syndrome reference "Nair, Pratibhu. Bulbar Palsy, Progressive, with Sensorineural Deafness. The Catalogue for Transmission Genetics in Arabs, CTGA Database. Centre for Arab Genomic Studies. www.cag.org.".
- Brown–Vialetto–Van_Laere_syndrome reference "Prabhu HV, and Brown MJK. Brown-Vialetto-Van Laere syndrome: a rare syndrome in otology – a case report and literature review. The Journal of Laryngology and Otology. 119: 470-472.".
- Brown–Vialetto–Van_Laere_syndrome reference "Sathasivam S, O’Sullivan S, Nicolson A, Tilley PJB, and Shaw PJ. Brown-Vialetto-Van Laere syndrome: Case report and literature review. ALS and Other Motor Neuron Disorders. 1:277-281.".
- Brown–Vialetto–Van_Laere_syndrome reference "Voudris KA, Skardoutsou A, and Vagiakou EA. Infantile progressive bulbar palsy with deafness. Brain and Development. 24:732-735.".
- Brown–Vialetto–Van_Laere_syndrome reference "Wilson, John Eastman. Diseases affecting the spinal grey-matter. Diseases of the Nervous System. Boericke and Runyon.".
- Brown–Vialetto–Van_Laere_syndrome subject Category:Neurological_disorders.
- Brown–Vialetto–Van_Laere_syndrome type Disease.
- Brown–Vialetto–Van_Laere_syndrome type Situation.
- Brown–Vialetto–Van_Laere_syndrome comment "Brown-Vialetto-Van-Laere syndrome (BVVL), sometimes better known as Brown's Syndrome, is a rare degenerative disorder that is characterized by progressive sensorineural deafness (Voudris 2002). BVVL is marked by a number of cranial nerve palsies including those of the motor components involving the 7th and 9th-12th cranial nerves, spinal motor nerves, and upper motor neurons (Voudris 2002).".
- Brown–Vialetto–Van_Laere_syndrome label "Brown–Vialetto–Van Laere syndrome".
- Brown–Vialetto–Van_Laere_syndrome label "Zespół Browna-Vialetto-Van Laerego".
- Brown–Vialetto–Van_Laere_syndrome sameAs Brown%E2%80%93Vialetto%E2%80%93Van_Laere_syndrome.
- Brown–Vialetto–Van_Laere_syndrome sameAs Zespół_Browna-Vialetto-Van_Laerego.
- Brown–Vialetto–Van_Laere_syndrome sameAs Q4976847.
- Brown–Vialetto–Van_Laere_syndrome sameAs Q4976847.
- Brown–Vialetto–Van_Laere_syndrome wasDerivedFrom Brown–Vialetto–Van_Laere_syndrome?oldid=603743648.