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- Carnitine_palmitoyltransferase_I abstract "Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase I, is a mitochondrial enzyme responsible for the formation of acyl carnitines by catalyzing the transfer of the acyl group of a long-chain fatty acyl-CoA from coenzyme A to l-carnitine. The product is often palmitoylcarnitine (thus the name), but other fatty acids may also be substrates. It is part of a family of enzymes called carnitine acyltransferases. This "preparation" allows for subsequent movement of the acyl carnitine from the cytosol into the intermembrane space of mitochondria. Three isoforms of CPT1 are currently known: CPT1A, CPT1B, and CPT1C. CPT1 is associated with the outer mitochondrial membrane. This enzyme can be inhibited by malonyl CoA. Its role in fatty acid metabolism makes CPT1 important in many metabolic disorders such as diabetes. Since its crystal structure is not known, its exact mechanism of action remains to be elucidated.".
- Carnitine_palmitoyltransferase_I arm "q".
- Carnitine_palmitoyltransferase_I band "13.1".
- Carnitine_palmitoyltransferase_I band "13.3".
- Carnitine_palmitoyltransferase_I band "13.33".
- Carnitine_palmitoyltransferase_I chromosome "11".
- Carnitine_palmitoyltransferase_I chromosome "19".
- Carnitine_palmitoyltransferase_I chromosome "22".
- Carnitine_palmitoyltransferase_I ecNumber "2.3.1.21".
- Carnitine_palmitoyltransferase_I entrezgene "126129".
- Carnitine_palmitoyltransferase_I entrezgene "1374".
- Carnitine_palmitoyltransferase_I entrezgene "1375".
- Carnitine_palmitoyltransferase_I hgncid "18540".
- Carnitine_palmitoyltransferase_I hgncid "2328".
- Carnitine_palmitoyltransferase_I hgncid "2329".
- Carnitine_palmitoyltransferase_I locusSupplementaryData "-13.5".
- Carnitine_palmitoyltransferase_I omim "600528".
- Carnitine_palmitoyltransferase_I omim "601987".
- Carnitine_palmitoyltransferase_I omim "608846".
- Carnitine_palmitoyltransferase_I refseq "NM_001876".
- Carnitine_palmitoyltransferase_I refseq "NM_152245".
- Carnitine_palmitoyltransferase_I refseq "NM_152359".
- Carnitine_palmitoyltransferase_I symbol "CPT1".
- Carnitine_palmitoyltransferase_I symbol "CPT1A".
- Carnitine_palmitoyltransferase_I symbol "CPT1B".
- Carnitine_palmitoyltransferase_I symbol "CPT1C".
- Carnitine_palmitoyltransferase_I thumbnail Carnitine_Acetyltransferase_and_Carnitine.png?width=300.
- Carnitine_palmitoyltransferase_I uniprot "P50416".
- Carnitine_palmitoyltransferase_I uniprot "Q8TCG5".
- Carnitine_palmitoyltransferase_I uniprot "Q92523".
- Carnitine_palmitoyltransferase_I wikiPageExternalLink br.fcgi?book=gene&part=cpt1a.
- Carnitine_palmitoyltransferase_I wikiPageID "10744662".
- Carnitine_palmitoyltransferase_I wikiPageRevisionID "596099304".
- Carnitine_palmitoyltransferase_I altsymbols "CPT1".
- Carnitine_palmitoyltransferase_I arm "q".
- Carnitine_palmitoyltransferase_I band "13.1".
- Carnitine_palmitoyltransferase_I band "13.3".
- Carnitine_palmitoyltransferase_I band "13.33".
- Carnitine_palmitoyltransferase_I chromosome "11".
- Carnitine_palmitoyltransferase_I chromosome "19".
- Carnitine_palmitoyltransferase_I chromosome "22".
- Carnitine_palmitoyltransferase_I ecnumber "2.3".
- Carnitine_palmitoyltransferase_I entrezgene "126129".
- Carnitine_palmitoyltransferase_I entrezgene "1374".
- Carnitine_palmitoyltransferase_I entrezgene "1375".
- Carnitine_palmitoyltransferase_I hasPhotoCollection Carnitine_palmitoyltransferase_I.
- Carnitine_palmitoyltransferase_I hgncid "18540".
- Carnitine_palmitoyltransferase_I hgncid "2328".
- Carnitine_palmitoyltransferase_I hgncid "2329".
- Carnitine_palmitoyltransferase_I locussupplementarydata "-13.5".
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1A".
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1B".
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1C".
- Carnitine_palmitoyltransferase_I omim "600528".
- Carnitine_palmitoyltransferase_I omim "601987".
- Carnitine_palmitoyltransferase_I omim "608846".
- Carnitine_palmitoyltransferase_I refseq "NM_001876".
- Carnitine_palmitoyltransferase_I refseq "NM_152245".
- Carnitine_palmitoyltransferase_I refseq "NM_152359".
- Carnitine_palmitoyltransferase_I symbol "CPT1A".
- Carnitine_palmitoyltransferase_I symbol "CPT1B".
- Carnitine_palmitoyltransferase_I symbol "CPT1C".
- Carnitine_palmitoyltransferase_I uniprot "P50416".
- Carnitine_palmitoyltransferase_I uniprot "Q8TCG5".
- Carnitine_palmitoyltransferase_I uniprot "Q92523".
- Carnitine_palmitoyltransferase_I type Biomolecule.
- Carnitine_palmitoyltransferase_I type Protein.
- Carnitine_palmitoyltransferase_I type ProteinMolecule.
- Carnitine_palmitoyltransferase_I type BiologicalObject.
- Carnitine_palmitoyltransferase_I comment "Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase I, is a mitochondrial enzyme responsible for the formation of acyl carnitines by catalyzing the transfer of the acyl group of a long-chain fatty acyl-CoA from coenzyme A to l-carnitine. The product is often palmitoylcarnitine (thus the name), but other fatty acids may also be substrates.".
- Carnitine_palmitoyltransferase_I label "Carnitina palmitoiltransferasa I".
- Carnitine_palmitoyltransferase_I label "Carnitine palmitoyltransferase I".
- Carnitine_palmitoyltransferase_I sameAs Carnitina_palmitoiltransferasa_I.
- Carnitine_palmitoyltransferase_I sameAs m.02qnw19.
- Carnitine_palmitoyltransferase_I sameAs Q5044069.
- Carnitine_palmitoyltransferase_I sameAs Q5044069.
- Carnitine_palmitoyltransferase_I wasDerivedFrom Carnitine_palmitoyltransferase_I?oldid=596099304.
- Carnitine_palmitoyltransferase_I depiction Carnitine_Acetyltransferase_and_Carnitine.png.
- Carnitine_palmitoyltransferase_I isPrimaryTopicOf Carnitine_palmitoyltransferase_I.
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1A (liver)".
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1B (muscle)".
- Carnitine_palmitoyltransferase_I name "carnitine palmitoyltransferase 1C (brain)".