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- Hypertrophic_cardiomyopathy abstract "Hypertrophic cardiomyopathy (HCM) is a primary disease of the myocardium (the muscle of the heart) in which a portion of the myocardium is hypertrophied (thickened) without any obvious cause. It is a leading cause of sudden cardiac death in young athletes.The occurrence of hypertrophic cardiomyopathy is a significant cause of sudden unexpected cardiac death in any age group and as a cause of disabling cardiac symptoms. Younger people are likely to have a more severe form of hypertrophic cardiomyopathy.[citation needed]HCM is frequently asymptomatic until sudden cardiac death, and for this reason some suggest routinely screening certain populations for this disease.A cardiomyopathy is a disease that affects the muscle of the heart. With HCM, the sarcomeres (contractile elements) in the heart increase in size, which results in the thickening of the heart muscle. In addition, the normal alignment of muscle cells is disrupted, a phenomenon known as myocardial disarray. HCM also causes disruptions of the electrical functions of the heart. HCM is most commonly due to a mutation in one of 9 sarcomeric genes that results in a mutated protein in the sarcomere, the primary component of the myocyte (the muscle cell of the heart). These are predominantly single-point missense mutations in the genes for beta-myosin heavy chain (MHC), myosin-binding protein C, cardiac troponinT, or tropomyosin. These mutations cause myofibril and myocyte structural abnormalities and possible deficiencies in force generation.While most literature so far focuses on European, American, and Japanese populations, HCM appears in all racial groups. The prevalence of HCM is about 0.2% to 0.5% of the general population.".
- Hypertrophic_cardiomyopathy diseasesdb "6373".
- Hypertrophic_cardiomyopathy emedicineSubject "med".
- Hypertrophic_cardiomyopathy emedicineTopic "290".
- Hypertrophic_cardiomyopathy icd10 "I42.1–I42.2".
- Hypertrophic_cardiomyopathy icd9 "425.4".
- Hypertrophic_cardiomyopathy medlineplus "000192".
- Hypertrophic_cardiomyopathy meshId "D002312".
- Hypertrophic_cardiomyopathy omim "192600".
- Hypertrophic_cardiomyopathy thumbnail Blausen_0166_Cardiomyopathy_Hypertrophic.png?width=300.
- Hypertrophic_cardiomyopathy wikiPageExternalLink br.fcgi?book=gene&part=hyper-card.
- Hypertrophic_cardiomyopathy wikiPageExternalLink cm.
- Hypertrophic_cardiomyopathy wikiPageID "606009".
- Hypertrophic_cardiomyopathy wikiPageRevisionID "604496580".
- Hypertrophic_cardiomyopathy align "'right'".
- Hypertrophic_cardiomyopathy caption "Illustration of Hypertrophic Cardiomyopathy".
- Hypertrophic_cardiomyopathy description "Echocardiogram demonstrating systolic anterior motion of the anterior leaflet of the mitral valve".
- Hypertrophic_cardiomyopathy diseasesdb "6373".
- Hypertrophic_cardiomyopathy emedicinesubj "med".
- Hypertrophic_cardiomyopathy emedicinetopic "290".
- Hypertrophic_cardiomyopathy filename "Hypertrophic Cardiomyopathy - Echocardiogram - Sam.ogg".
- Hypertrophic_cardiomyopathy format Ogg.
- Hypertrophic_cardiomyopathy hasPhotoCollection Hypertrophic_cardiomyopathy.
- Hypertrophic_cardiomyopathy icd "425.4".
- Hypertrophic_cardiomyopathy icd "I42.1–I42.2".
- Hypertrophic_cardiomyopathy medlineplus "192".
- Hypertrophic_cardiomyopathy meshid "D002312".
- Hypertrophic_cardiomyopathy name "Hypertrophic cardiomyopathy".
- Hypertrophic_cardiomyopathy omim "192600".
- Hypertrophic_cardiomyopathy title "Systolic anterior motion of the mitral valve".
- Hypertrophic_cardiomyopathy wordnet_type synset-disease-noun-1.
- Hypertrophic_cardiomyopathy subject Category:Autosomal_dominant_disorders.
- Hypertrophic_cardiomyopathy subject Category:Cardiogenetic_disorders.
- Hypertrophic_cardiomyopathy subject Category:Cardiomyopathy.
- Hypertrophic_cardiomyopathy subject Category:Cat_diseases.
- Hypertrophic_cardiomyopathy subject Category:Cytoskeletal_defects.
- Hypertrophic_cardiomyopathy type Disease.
- Hypertrophic_cardiomyopathy type AilmentCondition.
- Hypertrophic_cardiomyopathy type Situation.
- Hypertrophic_cardiomyopathy comment "Hypertrophic cardiomyopathy (HCM) is a primary disease of the myocardium (the muscle of the heart) in which a portion of the myocardium is hypertrophied (thickened) without any obvious cause. It is a leading cause of sudden cardiac death in young athletes.The occurrence of hypertrophic cardiomyopathy is a significant cause of sudden unexpected cardiac death in any age group and as a cause of disabling cardiac symptoms.".
- Hypertrophic_cardiomyopathy label "Cardiomiopatia hipertrófica".
- Hypertrophic_cardiomyopathy label "Cardiomiopatia ipertrofica".
- Hypertrophic_cardiomyopathy label "Cardiomyopathie hypertrophique".
- Hypertrophic_cardiomyopathy label "Hypertrofische obstructieve cardiomyopathie".
- Hypertrophic_cardiomyopathy label "Hypertrophe Kardiomyopathie".
- Hypertrophic_cardiomyopathy label "Hypertrophic cardiomyopathy".
- Hypertrophic_cardiomyopathy label "Kardiomiopatia przerostowa".
- Hypertrophic_cardiomyopathy label "Miocardiopatía hipertrófica".
- Hypertrophic_cardiomyopathy label "Гипертрофическая кардиомиопатия".
- Hypertrophic_cardiomyopathy label "اعتلال عضلة القلب الضخامي".
- Hypertrophic_cardiomyopathy label "肥大型心筋症".
- Hypertrophic_cardiomyopathy sameAs Hypertrophe_Kardiomyopathie.
- Hypertrophic_cardiomyopathy sameAs Miocardiopatía_hipertrófica.
- Hypertrophic_cardiomyopathy sameAs Cardiomyopathie_hypertrophique.
- Hypertrophic_cardiomyopathy sameAs Cardiomiopatia_ipertrofica.
- Hypertrophic_cardiomyopathy sameAs 肥大型心筋症.
- Hypertrophic_cardiomyopathy sameAs Hypertrofische_obstructieve_cardiomyopathie.
- Hypertrophic_cardiomyopathy sameAs Kardiomiopatia_przerostowa.
- Hypertrophic_cardiomyopathy sameAs Cardiomiopatia_hipertrófica.
- Hypertrophic_cardiomyopathy sameAs m.02vv4g.
- Hypertrophic_cardiomyopathy sameAs Q1364270.
- Hypertrophic_cardiomyopathy sameAs Q1364270.
- Hypertrophic_cardiomyopathy sameAs C0700053.
- Hypertrophic_cardiomyopathy wasDerivedFrom Hypertrophic_cardiomyopathy?oldid=604496580.
- Hypertrophic_cardiomyopathy depiction Blausen_0166_Cardiomyopathy_Hypertrophic.png.
- Hypertrophic_cardiomyopathy isPrimaryTopicOf Hypertrophic_cardiomyopathy.
- Hypertrophic_cardiomyopathy name "Hypertrophic cardiomyopathy".