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- Superior_mesenteric_artery_syndrome abstract "Superior mesenteric artery (SMA) syndrome is a very rare, life-threatening gastro-vascular disorder characterized by a compression of the third portion of the duodenum by the abdominal aorta (AA) and the overlying superior mesenteric artery. The syndrome is typically caused by an angle of 6°-25° between the AA and the SMA, in comparison to the normal range of 38°-56°, due to a lack of retroperitoneal and visceral fat. In addition, the aortomesenteric distance is 2-8 millimeters, as opposed to the typical 10-20.SMA syndrome was first described in 1861 by Carl Freiherr von Rokitansky in victims at autopsy, but remained pathologically undefined until 1927 when Wilkie published the first comprehensive series of 75 patients. Only 0.013 - 0.3% of upper-gastrointestinal-tract barium studies support a diagnosis, making it one of the rarest gastrointestinal disorders known to medical science. With only about 500 cases reported in the history of English-language medical literature, recognition of SMA syndrome as a distinct clinical entity is controversial, though it is now widely acknowledged. SMA syndrome is estimated to have a mortality rate of 1 in 3.SMA syndrome is also known as Wilkie's syndrome, cast syndrome, mesenteric root syndrome, chronic duodenal ileus and intermittent arterio-mesenteric occlusion.It is distinct from Nutcracker syndrome, which is the entrapment of the left renal vein between the AA and the SMA.".
- Superior_mesenteric_artery_syndrome emedicineSubject "article".
- Superior_mesenteric_artery_syndrome emedicineTopic "932220".
- Superior_mesenteric_artery_syndrome icd9 "557.1".
- Superior_mesenteric_artery_syndrome thumbnail Rokitansky_Carl.jpg?width=300.
- Superior_mesenteric_artery_syndrome wikiPageID "16740653".
- Superior_mesenteric_artery_syndrome wikiPageRevisionID "601246357".
- Superior_mesenteric_artery_syndrome caption "SMA syndrome was first described in 1861 by Carl Freiherr von Rokitansky.".
- Superior_mesenteric_artery_syndrome emedicinesubj "article".
- Superior_mesenteric_artery_syndrome emedicinetopic "932220".
- Superior_mesenteric_artery_syndrome hasPhotoCollection Superior_mesenteric_artery_syndrome.
- Superior_mesenteric_artery_syndrome icd "557.1".
- Superior_mesenteric_artery_syndrome name "SMA Syndrome".
- Superior_mesenteric_artery_syndrome wordnet_type synset-disease-noun-1.
- Superior_mesenteric_artery_syndrome subject Category:Causes_of_death.
- Superior_mesenteric_artery_syndrome subject Category:GI_tract_disorders.
- Superior_mesenteric_artery_syndrome subject Category:Medical_emergencies.
- Superior_mesenteric_artery_syndrome subject Category:Rare_diseases.
- Superior_mesenteric_artery_syndrome subject Category:Syndromes.
- Superior_mesenteric_artery_syndrome subject Category:Vascular_diseases.
- Superior_mesenteric_artery_syndrome type Abstraction100002137.
- Superior_mesenteric_artery_syndrome type Attribute100024264.
- Superior_mesenteric_artery_syndrome type Cognition100023271.
- Superior_mesenteric_artery_syndrome type Complex105870365.
- Superior_mesenteric_artery_syndrome type Concept105835747.
- Superior_mesenteric_artery_syndrome type Condition113920835.
- Superior_mesenteric_artery_syndrome type Content105809192.
- Superior_mesenteric_artery_syndrome type Crisis107417644.
- Superior_mesenteric_artery_syndrome type Disease114070360.
- Superior_mesenteric_artery_syndrome type Disorder114052403.
- Superior_mesenteric_artery_syndrome type Emergency107417405.
- Superior_mesenteric_artery_syndrome type Event100029378.
- Superior_mesenteric_artery_syndrome type GITractDisorders.
- Superior_mesenteric_artery_syndrome type Happening107283608.
- Superior_mesenteric_artery_syndrome type Idea105833840.
- Superior_mesenteric_artery_syndrome type IllHealth114052046.
- Superior_mesenteric_artery_syndrome type Illness114061805.
- Superior_mesenteric_artery_syndrome type Juncture107416714.
- Superior_mesenteric_artery_syndrome type MedicalEmergencies.
- Superior_mesenteric_artery_syndrome type PathologicalState114051917.
- Superior_mesenteric_artery_syndrome type PhysicalCondition114034177.
- Superior_mesenteric_artery_syndrome type PsychologicalFeature100023100.
- Superior_mesenteric_artery_syndrome type State100024720.
- Superior_mesenteric_artery_syndrome type Syndrome105870790.
- Superior_mesenteric_artery_syndrome type Syndromes.
- Superior_mesenteric_artery_syndrome type Whole105869584.
- Superior_mesenteric_artery_syndrome type YagoPermanentlyLocatedEntity.
- Superior_mesenteric_artery_syndrome type Disease.
- Superior_mesenteric_artery_syndrome type AilmentCondition.
- Superior_mesenteric_artery_syndrome type Situation.
- Superior_mesenteric_artery_syndrome comment "Superior mesenteric artery (SMA) syndrome is a very rare, life-threatening gastro-vascular disorder characterized by a compression of the third portion of the duodenum by the abdominal aorta (AA) and the overlying superior mesenteric artery. The syndrome is typically caused by an angle of 6°-25° between the AA and the SMA, in comparison to the normal range of 38°-56°, due to a lack of retroperitoneal and visceral fat.".
- Superior_mesenteric_artery_syndrome label "Sindrome dell'arteria mesenterica superiore".
- Superior_mesenteric_artery_syndrome label "Superior mesenteric artery syndrome".
- Superior_mesenteric_artery_syndrome label "متلازمة الشريان المساريقي العلوي".
- Superior_mesenteric_artery_syndrome label "上腸間膜動脈症候群".
- Superior_mesenteric_artery_syndrome sameAs Sindrome_dell'arteria_mesenterica_superiore.
- Superior_mesenteric_artery_syndrome sameAs 上腸間膜動脈症候群.
- Superior_mesenteric_artery_syndrome sameAs m.0404nm8.
- Superior_mesenteric_artery_syndrome sameAs Q1642206.
- Superior_mesenteric_artery_syndrome sameAs Q1642206.
- Superior_mesenteric_artery_syndrome sameAs 725.
- Superior_mesenteric_artery_syndrome sameAs Superior_mesenteric_artery_syndrome.
- Superior_mesenteric_artery_syndrome wasDerivedFrom Superior_mesenteric_artery_syndrome?oldid=601246357.
- Superior_mesenteric_artery_syndrome depiction Rokitansky_Carl.jpg.
- Superior_mesenteric_artery_syndrome isPrimaryTopicOf Superior_mesenteric_artery_syndrome.
- Superior_mesenteric_artery_syndrome name "SMA Syndrome".